What is nevus Lipomatosus Superficialis?
Nevus lipomatosus superficialis is an uncommon benign hamartomatous skin lesion defined by the presence of aggregates of mature adipose tissue among the collagen bundles of the dermis.
What causes nevus Lipomatosus?
The cause of the predilection of nevus lipomatosus superficialis for the pelvic girdle region is unknown. Theories of the predilection for pelvic girdle region include: Persistent pressure in the pelvic girdle area during intrauterine life.
What is a Collagenoma?
Collagenoma is a type of connective tissue nevi, a rare hamartomatous malformation characterized by the predominant proliferation of normal collagen fibers and normal, decreased, or increased elastic fibers.
What is intradermal nevus?
Intradermal melanocytic nevi are common, benign, pigmented skin tumors formed by proliferation of dermal melanocytes. A number of notable, uncommon changes may be observed in intradermal melanocytic nevi. In particular, their association with lymphatic invasion is an extremely rare phenomenon.
What causes connective tissue nevus?
A connective tissue naevus (American spelling nevus) is an uncommon skin lesion that occurs when the deeper layers of the skin do not develop correctly or the components of these layers occur in the wrong proportion. There may be too much collagen; this is called a collagenoma.
Is a nevus a hamartoma?
Nevus is defined as a type of hamartoma representing a circumscribed stable malformation of the skin that is not due to external causes and is presumed to be of hereditary origin.
What is an Elastoma?
Elastoma is a connective tissue nevus characterized by changes in elastic fibers. It can be congenital or acquired, and is usually diagnosed before puberty. Associated with osteopoikilosis, it is known as Buschke-Ollendorff syndrome.
What is the difference between a mole and a nevus?
A mole (nevus) is a non-cancerous (benign) skin lesion that is made up of the color-producing (pigment-producing) cells of the skin (melanocytes). A mole that is present at birth is referred to as a congenital nevus. A dysplastic nevus (discussed elsewhere) is a mole in which unusual (atypical) growth is noted.
What are 4 types of moles?
There are 4 common types of moles: congenital moles, dysplastic nevi, acquired nevi, and spitz nevi. Below are the differences between each.
What is connective tissue nevi?
Connective tissue nevi (CTN) are hamartomas of the dermis, with the 3 main components being collagen, elastin, and proteoglycans. Each subtype can present as a solitary lesion or multiple lesions. They could present as part of systemic diseases or inherited disorders.
What is the difference between hamartoma and benign tumor?
A hamartoma is a benign tumor that may occur in the lungs, heart, skin, brain, breast, or other regions. 1 They are made up of abnormal but not cancerous cells similar to the cells that make up the tissue where they originate.
What is an example of hamartoma?
The literature describes several examples of hamartomas, including the following: Hemangioma and other vascular tumors that are not true neoplasms. Peutz-Jeghers polyp of the bowel, juvenile or retention. Polyp of the large bowel.
What is nevus lipomatosus superficialis?
Nevus lipomatosus superficialis is an uncommon benign hamartomatous skin lesion defined by the presence of aggregates of mature adipose tissue among the collagen bundles of the dermis. It was first reported by Hoffman and Zurhelle in 1921.[1]
How is naevus lipomatosus superficialis diagnosed?
Naevus lipomatosus superficialis is diagnosed by histopathological examination of a skin biopsy. Mature adipose cells are found in the dermis and are not connected to the subcutaneous tissue where fat cells usually reside. What is the differential diagnosis of naevus lipomatosus superficialis?
How many types of naevus lipomatosus are there?
Two types are described: the classical type (also called Hoffmann-Zurhelle) and the solitary type. Other names for naevus lipomatosus superficialis are superficial lipomatous naevus and fat naevus.
What are the DSM-5 codes for keratosis?
White’s (congenital) (keratosis follicularis) 757.39 Dyskeratosis (see also Keratosis) 701.1 bullosa hereditaria 757.39 congenital 757.39 follicularis 757.39 vitamin A deficiency 264.8 Elastoma 757.39 juvenile 757.39 Miescher’s (elastosis perforans serpiginosa) 701.1